Orbital Tumors - Neurofibroma

General

• most common nerve sheath tumor
• hamartoma of endoneural fibroblasts, Schwann cells, axons
• localized
• present in early to middle age
• like schwannomas, 10% have NF1

Imaging

• not encapsulated but cannot tell from imaging

Pathology

Surgery

• can be multiple, plexiform (diffuse)
• remove by superior orbitotomy, can undergo malignant transformation